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La revue de médecine interne – Vol. 33 – N° S2 – p. AA – Fièvre récurrente: penser à la maladie de Caroli – EM|consulte. C’est une cause rare de cholestase chronique et de lithiases intrahépatiques. Nous rapportons deux cas de maladie de Caroli monolobaire. Request PDF on ResearchGate | Maladie de Caroli monolobaire. À propos de 12 cas | BackgroundCaroli’s disease is the dilatation of the segmental intrahepatic.

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Edit article Share article View revision history. The treatment depends on clinical features and the location of the biliary abnormality. Hepatomegaly, cirrhosis and portal hypertension with splenomegaly are also frequently reported to develop.

Prognosis is generally poor. The first symptoms typically include feverintermittent abdominal painand hepatomegaly. Rev Fr Etud Clin Biol. Archived September 29,at the Wayback Machine. Annular pancreas Accessory pancreas Johanson—Blizzard syndrome Pancreas divisum. Asphyxiating thoracic dysplasia basal body: Jacques Caroli, a gastroenterologistfirst described a rare carolii condition in in ParisFrance.

Fibrose hépatique congénitale.

Summary and related texts. Polycystic kidney disease Autosomal dominant polycystic kidney Autosomal recessive polycystic kidney Medullary cystic kidney disease Nephronophthisis Congenital cystic dysplasia.


The ductal plate is a layer of hepatic precursor cells that surround the portal venous branches, and is the anlage of the intrahepatic bile ducts. Links to PubMed are also available for Selected References. Prognosis depends on the clinical course and the risk of cholangiocarcinoma. Epidemiology Clinical presentation Pathology Radiographic features Treatment and prognosis History and etymology Differential diagnosis References Images: Clinical description Caroli disease can present at any age.

Case 3 Case 3. CS is often associated with recessive polycystic kidney disease see these terms. Caroli disease is a congenital disorder comprising of multifocal cystic dilatation of segmental intrahepatic bile ducts.

Fibrose hépatique congénitale.

Bowel gas and digestive habits make it difficult to obtain a clear sonogramso a CT scan is a good substitution. Check this box if you wish to receive a copy of your message. This article has catoli cited by other articles in PMC. Cutaneous columnar cyst Keratin implantation cyst Verrucous cyst Adenoid cystic carcinoma Breast cyst.

Caroli disease

Full text Full text is available as a scanned copy of the original print version. Some patients remain asymptomatic throughout the disease course. From Wikipedia, the free encyclopedia. Ann Chir Thorac Cardiovasc.


Pyloric stenosis Carolu hernia. In a year period between andonly 10 patients were surgically treated for Caroli disease, with an average patient age of Support Radiopaedia and see fewer ads. Creative Commons Attribution 4. After reviewing 46 cases of Caroli disease before Journal of the Pancreas. Medical College of Wisconsin.

Caroli disease – Wikipedia

Antibiotics are used for cholangitis. Outline Masquer le plan. On a CT scan, Caroli disease can be observed by noting the many fluid-filled, tubular structures extending to the liver. Mladie Data Supplementary Materials.

Recurrent pyogenic cholangitis Recurrent pyogenic cholangitis. Thus, the simple type of Caroli disease results from the abnormal development of the large bile ducts.

Morbidity is common and is caused by complications of cholangitis, sepsiscarooliand cholangiocarcinoma. Acta Paediatr Acad Sci Hung.

National Center for Biotechnology InformationU. Journal page Archives Contents list.

Regular follow-ups, including ultrasounds and liver biopsies, are performed.